P-183 LYSINE ADMINISTRATION PROMOTES OXIDATIVE STRESS IN BRAIN OF GLUTARYL-COA DEHYDROGENASE-DEFICIENT (GCDH−/−) MICE 2011
Background: The pathogenesis of the brain damage in glutaric acidemia type I (GA I) is not well understood. Objectives: Relevant oxidative stress parameters were investigated in cerebral cortex, striatum, hippocampus, liver and heart of 30-day-old knockout mice with glutaryl-CoA dehydrogenase deficiency (Gcdh −/−) and in...